8711/3 Glomus tumor, malignant


Connective, subcutaneous and other soft tissues
ICD-O-3 topography code: C49
ICD10: C49

Malignant glomus tumour is an exceedingly rare morphologic variant of glomus tumour with a size >2 cm. The tumour arises in subfascial or visceral tissues and is histopathologically characterized by the presence of atypical mitotic figures, or marked nuclear atypia, or a combination of both. Malignant glomus tumours are highly aggressive. Approximately 40% of cases metastasize, resulting in the death of the patient 1
Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002