8623/1 Sex cord tumor with annular tubules


ICD-O-3 topography code: C56

An ovarian sex cord-stromal tumor characterized by the presence of Sertoli cells forming annular tubules and such cases usually have a benign clinical course.
About one-third of cases occur in women with Peutz-Jeghers syndrome (PJS) . The average age of patients with PJS is in the mid-twenties and of those not associated with PJS in the mid-thirties 1
Tavassoli FA, Devilee P (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Breast and Female Genital Organs.
3rd Edition
IARC Press: Lyon 2003