9444/1 Chordoid glioma of third ventricle

Related terms

Chordoid glioma


Tumours of the central nervous system
ICD-O-3 topography code: C70, C71 and C72

A rare, slow-growing neuroepithelial neoplasm of uncertain origin affecting adults. It is located in the third ventricle and histologically characterized by the presence of epithelioid cells which express GFAP, and mucinous stroma that contains lymphoplasmacytic infiltrates 1
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Brat DJ, Scheithauer BW, Staugaitis SM, Cortez SC, Brecher K, Burger PC (1998)
Third ventricular chordoid glioma: a distinct clinicopathologic entity.
J Neuropathol Exp Neurol 57: 283-90

Louis DN, Ohgaki H, Wiestler OD, Cavenee WK (Eds.)
WHO Classification of Tumours of the Central Nervous System.
4th Edition
International Agency for Research on Cancer: Lyon 2007

The tumour is well delineated, and shows strong contrast enhancement. Due to its attachment to hypothalamic structures, complete surgical resection is often not possible.