Synonyms

Rathke pouch tumor

Definitions

Tumours of the central nervous system
ICD-O-3 topography code:	C70, C71 and C72

A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms:
Adamantinomatous craniopharyngioma
Papillary craniopharyngioma
Recent studies indicate that the age distribution and, to some extent, prognosis are different between these two variants ¹

Louis DN, Ohgaki H, Wiestler OD, Cavenee WK (Eds.)
WHO Classification of Tumours of the Central Nervous System.
4th Edition
International Agency for Research on Cancer: Lyon 2007

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Bone
ICD-O-3 topography code:	C40-C41

A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. Recent studies indicate that the age distribution and, to some extent, prognosis are different between these two variants {34}.

Nasopharynx
ICD-O-3 topography code:	C11

A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. Recent studies indicate that the age distribution and, to some extent, prognosis are different between these two variants {34}.