9330/3 Ameloblastic sarcoma



Definitions

Bone
ICD-O-3 topography code: C40-C41
ICD10: C40-C41
           

A locally aggressive malignant neoplasm arising from odontogenic tissue. It occurs in the mandible and less often in the maxilla 1
 
Barnes L, Eveson JW, Reichart P, Sidransky D (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Head and Neck Tumours.
3rd Edition
IARC Press: Lyon 2005



. It is characterized by the presence of a malignant connective tissue component and a benign epithelial component. The frequency of distal metastases is low.