Synonyms

Ameloblastic fibrodentinosarcoma
Ameloblastic fibro-odontosarcoma

Definitions

Bone
ICD-O-3 topography code:	C40-C41
ICD10:	C40-C41

A locally aggressive malignant neoplasm arising from odontogenic tissue. It occurs in the mandible and less often in the maxilla. It is characterized by the presence of a malignant connective tissue component and a benign epithelial component. The frequency of distal metastases is low.