9252/3 Malignant tenosynovial giant cell tumor


Giant cell tumor of tendon sheath, malignant


Connective, subcutaneous and other soft tissues
ICD-O-3 topography code: C49
ICD10: C49

An uncommon malignant tumor arising from the tendon sheath. Morphologically, it is characterized by the presence of a cellular infiltrate reminiscent of a giant cell tumor with prominent malignant characteristics. Recurrent giant cell tumors with a sarcomatous dedifferentiation are included in this category as well.