9221/3 Periosteal chondrosarcoma


ICD-O-3 topography code: C40-C41
ICD10: C40-C41

A rare variant of chondrosarcoma, arising from hyaline cartilage on the surface of bone. It occurs preferentially in the long bones of adults. Clinical presentation includes pain, and sometimes swelling. It is histologically characterized by a lobulated growth pattern, high mitotic activity, myxoid stroma formation, and necrotic changes 1
Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002