9140/3 Multiple hemorrhagic sarcoma


Related terms

Kaposi sarcoma

Definitions

Tumours of the central nervous system
ICD-O-3 topography code: C70, C71 and C72
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS).



Liver and intrahepatic bile ducts
ICD-O-3 topography code: C22
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS). Disseminated Kaposi sarcoma involving the liver is usually an incidental finding on autopsy detected in 15% of patients with AIDS.

Hepatic Kaposi sarcoma typically involves portal and periportal areas, often grossly detectable as red-brownish foci. Histologically, these tumours typically show poorly vasoformative spindle-cell proliferation accompanied by haemorrhage and focal deposition of haemosiderin. Cytoplasmic eosinophilic hyaline globules are a typical finding, and immunohistochemical demonstration of membranous/cytoplasmic CD31 and CD34, and nuclear human herpesvirus 8 (HHV-8) are diagnostic 1
Click to access Pubmed
Noel JC, Hermans P, Andre J, Fayt I, Simonart T, Verhest A, Haot J, Burny A (1996)
Herpesvirus-like DNA sequences and Kaposi's sarcoma: relationship with epidemiology, clinical spectrum, and histologic features.
Cancer 77: 2132-6



2
 
Bosman FT, Carneiro F, Hruban RH, Theise ND (Eds.)
WHO Classification of Tumours of the Digestive System.
4th Edition
International Agency for Research on Cancer: Lyon 2010



.



Colon and rectum
ICD-O-3 topography code: C18-C20
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS).



Connective, subcutaneous and other soft tissues
ICD-O-3 topography code: C49
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS).



Stomach
ICD-O-3 topography code: C16
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS).



Gallbladder and extrahepatic biliary tract
ICD-O-3 topography code: C23-C24.0
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS).



Hypopharynx, Larynx and Trachea
ICD-O-3 topography code: C13, C32, C33
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS).



Lip, Oral Cavity and Oropharynx
ICD-O-3 topography code: C00-C06, C09-C10, C14
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS).



Small intestine
ICD-O-3 topography code: C17
ICD10: C46
           

A malignant neoplasm characterized by a vascular proliferation which usually contains blunt endothelial cells. Erythrocyte extravasation and hemosiderin deposition are frequently present. It preferentially develops in people with compromised immune systems including those with the acquired immune deficiency syndrome (AIDS).