8800/3 Soft tissue sarcoma


Related terms

Sarcoma, NOS

Definitions

Connective, subcutaneous and other soft tissues
ICD-O-3 topography code: C49
ICD10: C49
           

A usually aggressive malignant mesenchymal cell tumor most commonly arising from muscle, fat, fibrous tissue, bone, cartilage, and blood vessels. Sarcomas occur in both children and adults. The prognosis depends largely on the degree of differentiation (grade) of the tumor.

Representative subtypes include 1
 
Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002



:
Liposarcoma
Leiomyosarcoma
Osteosarcoma
Chondrosarcoma



Bronchus and lung
ICD-O-3 topography code: C34
ICD10: C34
           

Sarcomas of the large pulmonary arteries occur in two types. (1) Intimal sarcomas have an intraluminal polypoid growth pattern and usually show fibroblastic or myofibroblastic differentiation. (2) Mural sarcomas are are classified according to the histologic subtype, leiomyosarcomas being most frequent
2
 
Travis WD, Brambilla E, Müller-Hermelink HK, Harris CC (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Lung, Pleura, Thymus and Heart.
3rd Edition
IARC Press: Lyon 2004



.

Pulmonary vein sarcomas almost always shows features of leiomyosarcoma
3
 
Travis WD, Brambilla E, Müller-Hermelink HK, Harris CC (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Lung, Pleura, Thymus and Heart.
3rd Edition
IARC Press: Lyon 2004



.