9560/3 Neurilemoma, malignant


Synonyms

Malignant schwannoma, NOS
Neurilemosarcoma

Definitions

An uncommon, highly aggressive malignant tumor, arising from the peripheral nerves and affecting mostly adults in their third to sixth decades of life. It usually occurs in medium-sized and large nerves of the buttock, thigh, upper arm, or the paraspinal region. It may be associated with neurofibromatosis 1 (NF1).

This diagnostic term is not contained in the 2007 WHO Classification of Tumours of the Central Nervous System 1
 
Louis DN, Ohgaki H, Wiestler OD, Cavenee WK (Eds.)
WHO Classification of Tumours of the Central Nervous System.
4th Edition
International Agency for Research on Cancer: Lyon 2007



. The current term is malignant peripheral nerve sheath tumor (MPNST).