9491/0 Ganglioneuromatosis


Definitions

Gallbladder and extrahepatic biliary tract
ICD-O-3 topography code: C23-C24.0

Extensive and diffuse infiltration of tissues by ganglioneuroma.

Ganglioneuromatosis of the gallbladder and extrahepatic bile ducts
Diffuse ganglioneuromatosis can involve the gallbladder in patients with multiple endocrine neoplasia type 2B (MEN2B) OMIM . The lesions contain Schwann-cell elements admixed with scattered ganglion cells involving the entire wall of the gallbladder 1
Click to access Pubmed
Carney JA, Sizemore GW, Hayles AB (1978)
Multiple endocrine neoplasia, type 2b.
Pathobiol Annu 8: 105-53



. Diffuse or plexiform neurofibromas can also involve the biliary tract in patients with neurofibromatosis type 1 (NF1) OMIM 2
Click to access Pubmed
Mitchell DI, Char G, McDonald A, Scott P (1995)
Plexiform neurofibroma: a rare cause of obstructive jaundice.
West Indian Med J 44: 146-7



3
 
Bosman FT, Carneiro F, Hruban RH, Theise ND (Eds.)
WHO Classification of Tumours of the Digestive System.
4th Edition
International Agency for Research on Cancer: Lyon 2010



.



Tumours of the central nervous system
ICD-O-3 topography code: C70, C71 and C72

Extensive and diffuse infiltration of tissues by ganglioneuroma.