9423/3 Polar spongioblastoma


Synonyms

Spongioblastoma polare
Primitive polar spongioblastoma

Definitions

Tumours of the central nervous system
ICD-O-3 topography code: C70, C71 and C72
ICD10: C71
           

Polar spongioblastoma was originally defined as a rare, benign glioma histopathologically characterized by symmetrical palisading of tumor cell nuclei on the background of a fibrillary matrix.
In 1999, a WHO Working Group recommended to delete 'polar spongioblastoma' from the WHO classification 1
 
Kleihues P, Cavenee WK (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Nervous System.
3rd Edition
IARC Press: Lyon 2000



, since it is not a well-defined clinicopathological entity and the palisading pattern typical for this lesion is observed in several other brain tumors, notably oligodendrogliomas.