9413/0 Dysembryoplastic neuroepithelial tumor


Definitions

Tumours of the central nervous system
ICD-O-3 topography code: C70, C71 and C72

A benign glial-neuronal neoplasm that occurs in children and young adults with a long-standing history of partial seizures. It is usually located in the cerebral cortex and is characterized by a complex nodular architecture. A histologic hallmark of this tumor is the 'specific glioneuronal element' 1
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Daumas-Duport C (1993)
Dysembryoplastic neuroepithelial tumours.
Brain Pathol 3: 283-95



, characterized by columns, made up of bundles of axons, oriented perpendicularly to the cortical surface. The prognosis following surgical resection is very favourable, without evidence of recurrence 2
 
Louis DN, Ohgaki H, Wiestler OD, Cavenee WK (Eds.)
WHO Classification of Tumours of the Central Nervous System.
4th Edition
International Agency for Research on Cancer: Lyon 2007



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