9391/3 Ependymoma, NOS


Synonyms

Epithelial ependymoma


Definitions

Tumours of the central nervous system
ICD-O-3 topography code: C70, C71 and C72
ICD10: C71
           

A slowly growing brain tumor of children and young adults, derived from the ependymal lining of the cerebral ventricles. Clinical symptoms typically result from blocking cerebrospinal fluid pathways. Key histological features include perivascular pseudorosettes and ependymal rosettes 1
 
Louis DN, Ohgaki H, Wiestler OD, Cavenee WK (Eds.)
WHO Classification of Tumours of the Central Nervous System.
4th Edition
International Agency for Research on Cancer: Lyon 2007



.

Histological variants of ependymoma:
Cellular ependymoma
Papillary ependymoma
Clear cell ependymoma
Tanycytic ependymoma



Ovary
ICD-O-3 topography code: C56
ICD10: C56
           

A slowly growing brain tumor of children and young adults, derived from the ependymal lining of the cerebral ventricles. Clinical symptoms typically result from blocking cerebrospinal fluid pathways. Key histological features include perivascular pseudorosettes and ependymal rosettes
2
 
Louis DN, Ohgaki H, Wiestler OD, Cavenee WK (Eds.)
WHO Classification of Tumours of the Central Nervous System.
4th Edition
International Agency for Research on Cancer: Lyon 2007



.



Fallopian tube and Uterine ligaments
ICD-O-3 topography code: C57
ICD10: C57
           

A slowly growing brain tumor of children and young adults, derived from the ependymal lining of the cerebral ventricles. Clinical symptoms typically result from blocking cerebrospinal fluid pathways. Key histological features include perivascular pseudorosettes and ependymal rosettes
3
 
Louis DN, Ohgaki H, Wiestler OD, Cavenee WK (Eds.)
WHO Classification of Tumours of the Central Nervous System.
4th Edition
International Agency for Research on Cancer: Lyon 2007



.

Only a few ependymomas have been described in the uterine ligaments and the broad ligament. Patients were 13-48 years of age with a mean of 38 years and presented with a mass associated with lower quadrant tenderness
4
 
Tavassoli FA, Devilee P (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of the Breast and Female Genital Organs.
3rd Edition
IARC Press: Lyon 2003



.