9290/3 Ameloblastic odontosarcoma
|ICD-O-3 topography code:||C40-C41|
A locally aggressive malignant neoplasm arising from odontogenic tissue. It occurs in the mandible and less often in the maxilla. It is characterized by the presence of a malignant connective tissue component and a benign epithelial component. The frequency of distal metastases is low.