9121/0 Cavernous hemangioma


Definitions

Liver and intrahepatic bile ducts
ICD-O-3 topography code: C22

A hemangioma characterized by the presence of cavernous vascular spaces.

Hepatic cavernous haemangioma
This is the most common benign tumour of the liver 1
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Bioulac-Sage P, Laumonier H, Laurent C, Blanc JF, Balabaud C (2008)
Benign and malignant vascular tumors of the liver in adults.
Semin Liver Dis 28: 302-14



. The reported incidence varies from 0.4% to 20% in autopsy studies, the highest figure being the result of a thorough prospective search 2
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Karhunen PJ (1986)
Benign hepatic tumours and tumour like conditions in men.
J Clin Pathol 39: 183-8



. It occurs at all ages, but is more commonly seen in young adult females. It is known to increase in size or even rupture during pregnancy, and also may enlarge or recur in patients on estrogen therapy. Haemangiomas are symptomatic only when they are > 4 cm in size, leading to pain or a mass syndrome. Rupture or acute thrombosis are exceptional, as well as the severe Kasaback-Merritt syndrome with consumptive coagulopathy 3
 
Bosman FT, Carneiro F, Hruban RH, Theise ND (Eds.)
WHO Classification of Tumours of the Digestive System.
4th Edition
International Agency for Research on Cancer: Lyon 2010



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Connective, subcutaneous and other soft tissues
ICD-O-3 topography code: C49

A hemangioma characterized by the presence of cavernous vascular spaces.