8900/0 Rhabdomyoma, NOS


Definitions

Tumours of the central nervous system
ICD-O-3 topography code: C70, C71 and C72

Rhabdomyoma (RM) is a benign neoplasm arising from striated muscle. It is composed of cytologically bland, delicate fetal myotubules in a myxoid stroma. There may be an admixture of rhabdomyoblasts.

Extracardiac RM is subclassified into adult rhabdomyoma and fetal rhabdomyoma, according to the degree of differentiation, and predominantly affects the head and neck region. Rare cases of extracardiac RM arise in the genital tract (genital rhabdomyoma)1
 
Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002



.



Connective, subcutaneous and other soft tissues
ICD-O-3 topography code: C49

Rhabdomyoma (RM) is a benign neoplasm arising from striated muscle. It is composed of cytologically bland, delicate fetal myotubules in a myxoid stroma. There may be an admixture of rhabdomyoblasts.

Extracardiac RM is subclassified into adult rhabdomyoma and fetal rhabdomyoma, according to the degree of differentiation, and predominantly affects the head and neck region. Rare cases of extracardiac RM arise in the genital tract (genital rhabdomyoma)
2
 
Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002



.



Hypopharynx, Larynx and Trachea
ICD-O-3 topography code: C13, C32, C33

Rhabdomyoma (RM) is a benign neoplasm arising from striated muscle. It is composed of cytologically bland, delicate fetal myotubules in a myxoid stroma. There may be an admixture of rhabdomyoblasts.

Extracardiac RM is subclassified into adult rhabdomyoma and fetal rhabdomyoma, according to the degree of differentiation, and predominantly affects the head and neck region. Rare cases of extracardiac RM arise in the genital tract (genital rhabdomyoma)
3
 
Fletcher CDM, Unni KK, Mertens F (Eds.)
World Health Organization Classification of Tumours. Pathology and Genetics of Tumours of Soft Tissue and Bone.
3rd Edition
IARC Press: Lyon 2002



.